Oral Health For Children With Cerebral Palsysee
photo
Cerebral palsy is the most common handicapping disorder in the United States. It
is a disorder of movement and posture caused by brain damage which occurs the
early stages of development. Cerebral palsy cannot be cured, but it does not get
worse with time. Approximately half of all children with cerebral palsy at their
first birthday “outgrow” signs of the disorder by their seventh birthday.
OVERVIEW
Cerebral palsy is not a single disease, but a group of disorders that
occur when a baby’s brain is damaged.
There are more than 100,000 children and adolescents in the U.S. who have
cerebral palsy.
The prevalence of severe C.P. is around 2 for every 1,000 live births.
The total annual cost of cerebral palsy to the United States is $5
billion.
WHAT ARE THE TYPES OF CEREBRAL PALSY?
Cerebral palsy may be classified according to the resulting problems with
posture and control of movement.
The classifications are: spastic, hypotonic, and athethotic.
Spastic: above-normal tone or stiffness of the muscles of the body.
Hypotonic: weak, “floppy,” lacking normal muscle tone.
Athetotic: slow, writhing, involuntary movements of hands and feet.
Athetosis is caused by problems in the extrapyramidal system of the brain.
Cerebral palsy may also be classified according to the motor disability
associated with it, such as:
hemiplegia, diplegia, dyskinesia, and quadriplegia.
Spastic hemiplegia: one-sided neurologic defect. The arm is more affected
than the leg.
Spastic diplegia: scissoring walking pattern, with toe-walking.
Dyskinesia: difficulty walking, with some spasticity.
Spastic quadriplegia: all limbs are affected, with multiple medical
complications.
WHAT CAUSES CEREBRAL PALSY?
The cause of cerebral palsy is poorly understood, but it is most likely
caused by a variety of factors.
Cerebral palsy can be associated with prenatal, perinatal, or postnatal
events.
Prenatal factors cause 70-80% of cases of cerebral palsy. The developing
brain is subject to injury at any time, due of its complexity and
vulnerability.
The most common finding in children with cerebral palsy is prenatal injury
to the portion of the brain lying next to the middle cerebral artery.
The clinical finding of prenatal brain injury - leukomalacia - predicts
cerebral palsy better than the ultrasonic finding of intracranial
hemorrhage. Periventricular leukomalacia is the medical term used to
describe death of the white matter of the brain in the area of the lateral
ventricles.
Recent studies have shown that difficulties during birth and delivery are
not a common cause of cerebral palsy.
WHAT ARE THE PRENATAL RISK FACTORS FOR CEREBRAL PALSY?
Prematurely born infants have a higher incidence of cerebral palsy than
babies born at term.
The rate of cerebral palsy is at least 25 times higher among infants who
weigh less than 1,500 g at birth, compared to full-sized newborns.
Any infection of the pregnant mother, such as rubella (German measles) or
dental infection, causes a risk to the unborn child.
Maternal drug or alcohol abuse.
Maternal thyroid disorder.
HOW IS CEREBRAL PALSY DIAGNOSED?
After birth, ultrasonic examination of the brain of a premature infant may
reveal cerebral abnormalities, such as hyperechoic and hypoechoic lesions.
After birth, hypoechoic areas which appear on ultrasonic images of a
baby’s brain can predict future problems, such as motor dysfunction
related to movement and coordination.
A physical examination of an infant with cerebral palsy may reveal:
spasticity of the limbs,
arms or legs which appear to be locked in an abnormal position,
lack of normal balance,
or an abnormal walking pattern in older children.
A large portion of children with cerebral palsy experience significant
feeding and swallowing problems during the first 12 months of life. This
finding often preceeds the diagnosis of cerebral palsy.
HOW IS CEREBRAL PALSY TREATED?
Cerebral palsy cannot be cured, but the most important part of therapy is
maintaining current function, and developing new function.
Treatment usually includes a combination of:
speech therapy,
occupational therapy,
prescription drugs,
surgery,
and counseling.
Rehabilitation medicine (physiatry) can help manage spasticity and
coordinate therapy.
Medication may relieve movement difficulties and spasticity. Baclofen and
diazepam are two examples of such medications.
Anticonvulsants are used to control seizures.
Intramuscular neurolysis using phenol, and intramuscular blocks using
botulinum A toxoid (Botox), may reduce spasticity.
Neurosurgery can help decrease spasticity by cutting 1-a sensory nerve
fibers (selective dorsal rhizotomy procedure).
HEALTH PROBLEMS IN CHILDREN WITH CEREBRAL PALSY
Thirty percent of children with cerebral palsy have some degree of mental
retardation
Twenty-five percent cannot walk.
Approximately one third of children with cerebral palsy have epilepsy. Up
to fifty percent of children with hemiplegic cerebral palsy have epilepsy.
Many children experience failure to thrive, due to feeding and swallowing
problems.
SPECIAL ORAL AND DENTAL HEALTH CONCERNS FOR CHILDREN WITH CEREBRAL PALSY
Orofacial dysfunction is a severe health problem, as well as a problem for
acceptance by peers and society.
Cerebral palsied children have drooling, eating, drinking, and speaking
disorders.
More than 90% of children with cerebral palsy have oral motor dysfunction.
The severity of oral dysfunction makes it difficult for some cerebral
palsied children to be adequately nourished.
Drooling is not due to excessive production of saliva, but to a poor and
disorganized swallowing pattern.
There is abnormal neuromuscular coordination of the tongue, lips, and
cheeks - which leads to poor dental alignment and periodontal problems.
Trauma of the face and mouth occur much more frequently in children who
have cerebral palsy.
Children with cerebral palsy may demonstrate self injurious behavior,
including:
tongue, cheek, and lip biting;
finger, arm, and hand chewing.
Protective oral appliances may be useful in combating self-injurious
behavior.
Children who are affected by cognitive disability or mental retardation
often practice damaging oral habits, including:
bruxism, rumination, pouching, and pica.
Bruxism:
This is clenching, grinding, and gnashing of teeth. It is a frequent finding
in children with cerebral palsy. The treatment for bruxism may include the
use of a soft or hard mouth guard – if the child can tolerate it.
Rumination:
this is the re-chewing, regurgitation, and re-swallowing of previously
ingested food. This habit causes the acidic contents of the stomach to
travel up into the mouth, and bathe the teeth in acid. Rumination can lead
to demineralization, and loss of tooth structure.
Pouching:
This is the placement of food or medicine between the cheek and teeth for a
long period of time. This habit can cause dental decay.
Pica:
This is the compulsive eating of non-edible substances, including: sand,
dirt, and paint chips. Pica can lead to destruction of tooth structure and
damage of oral soft tissue.
ORAL FINDINGS IN CHILDREN WITH CEREBRAL PALSY
Children with cerebral palsy frequently have gastroesophageal reflux, as
well as episodes of vomiting. Either problem can lead to dental erosion, or
loss of tooth structure.
Gingival overgrowth, due to seizure medications, is a frequent problem in
children with cerebral palsy.
Orofacial findings in spastic cerebral palsy:
The head is tensely reclined.
The mouth is open, and facial movements are tense.
The tongue is hypertonic and cigar-shaped.
There is tongue thrust during swallowing and speaking.
Since the upper lip is underdeveloped, it does not produce enough pressure
on the front teeth to align them correctly.
Orofacial findings in athetotic cerebral palsy:
The tongue shows spontaneous wave-like movements.
There may be an abrupt and wide opening of the mouth, which can lead to jaw
dislocation.
There is an uncoordinated movement of tongue, jaw, and face muscles.
Orofacial findings in hypotonic cerebral palsy:
The tongue is large, flat, and protruded.
Facial movements are weak, and the upper lip is inactive.
THE ROLE OF THE DENTIST
The dentist should try to schedule appointments for children with cerebral
palsy early in the day.
Obtain the child’s medical history before the first appointment so that
any necessary medical consultations can be arranged.
Try to develop a good rapport with the child.
Gain the cooperation of the cerebral palsied child by using behavior
management techniques such as: tell-show-do, positive reinforcement, and
voice control.
A child with severe cognitive disability may require repetition of
commands and requests, which will enhance comprehension.
A child with severe visual impairment needs a verbal description of the
planned dental procedures. This will help prevent fear and anxiety.
Communication can also be accomplished using nonverbal techniques,
especially for children with hearing impairment
The dentist may need to use sedation techniques to calm a child – if the
child’s medical situation permits. Some children can only be treated under
general anesthesia, however.
Children with cerebral palsy may have a severe gag reflex – making it
difficult to take dental radiographs.
Two modified radiographic techniques for use in children with cerebral
palsy are:
the 45 degree oblique head plate, and the reverse bite wing (buccal
technique).
In the oblique plate radiographic technique:
a film cassette is held against the patient’s cheek. The patient’s had
is rotated and tilted. The x-ray cylinder is placed just inferior and
posterior to the angle of the mandible on the opposite side of the face.
In the buccal bite wing technique:
the film packet is placed between the teeth and the cheek. The x-ray
cylinder is then placed below the lower border of the mandible on the
opposite side of the face.
When dental treatment is performed, stainless steel crowns are often used
when the posterior teeth have caries.
Fixed bridgework is usually not done for patients with cerebral palsy
because of the increased risk of falling and dental injury. Patients with
frequent seizures should normally not have fixed bridgework done because of
the possibility of damage to the supporting teeth or bone during a
seizure-related fall.
The dentist should discuss the option of myofunctional therapy for young
children who have orofacial and tongue hypotonia. This treatment may
increase the muscle tone of the lips, as well as keep the tongue inside of
the mouth.
The dentist should instruct parents on proper home dental hygiene
procedures.
Counsel parents about growth and development of the teeth and orofacial
structures.
Provide relevant dietary counseling.
Periodic dental recall appointments are highly recommended in order to
supervise and evaluate a patient’s oral hygiene. Recall appointments also
allow the dentist to monitor any gingival overgrowth which may be caused by
anti-seizure medications.
HOME DENTAL CARE FOR CHILDREN WITH CEREBRAL PALSY
Choose a well-lit location so that you can look into your child's mouth.
No matter what position you are using for brushing your child's teeth,
remember to always support the head.
Give lots of praise while brushing your child's teeth.
Parents should help brush their children's teeth every day, after every
meal. Brush the tongue, since this will help prevent halitosis.
Parents can help make children's teeth more decay-resistant by using an
ADA-approved children's toothpaste. Place only a pea-sized drop of
toothpaste on the toothbrush.
Up to the age of three, parents should only use baby tooth cleanser – to
avoid fluorosis discoloration of the adult teeth.
Children taking oral medications should have their teeth cleansed after
each dose of medication. Nearly 100% of children's medications contain
sucrose, which can increase the risk of developing dental caries.
Children should have their first oral/dental health evaluation by the age
of 12 months, or within 6 months of the eruption of the first tooth.
Parents should not let their children drink fruit juice or sweetened
drinks from a bottle or "tippy" cup, since this prolongs the
exposure of teeth to harmful sugar.
Parents should provide healthy, balanced meals for children. Plenty of
healthy snacks should be available for children. They should limit the
amount of sugar-laden foods and snacks in the diet. Cheese products actually
fight dental caries.
DOES OROFACIAL REGULATION THERAPY HELP?
The orofacial regulation therapy concept includes:
functional diagnostics of oral sensorimotor dysfunctions;
a special manual stimulation and facilitation program, which helps to
control and improve head and body posture;
the use of removable activating palatal plates, and other orthodontic
appliances.
Treatment using these activating orthodontic appliances should only be
done in conjunction with a special physiotherapy program.
Description of the myofunctional appliance for spasticity:
It includes a stimulating palatal plate, which helps to reduce tongue
thrust.
This removable appliance is worn every day, about one hour at a time, for a
total of four hours each day. This “palatal button” appliance is not
worn during sleep or feeding, however.
This appliance may be modified, later on, to include upper lip stimulators.
Description of the myofunctional appliance for hypotonia:
It acts by stimulating the facial “motor points.”
The upper lip may be stimulated with “bumpers” which are attached to a
“vestibular wire.”
CONCLUSION
Parents and caretakers should seek out physical, occupational, speech,
dental, and other professional therapists.
One organization which can provide additional assistance is:
The United Cerebral Palsy Associations,
1660 L Street NW,
Suite 700,
Washington DC 20036,
1-800-872-5827,
http://www.ucpa.org
An article in Pediatric Dentistry described an intraoral
appliance which decreases drooling in children who have cerebral palsy. The
appliance resembles an orthodontic retainer, which has a movable rolling
bead. The bead is attached at the posterior aspect of the appliance.
The myofunctional appliance described in the journal article is a
modification of the original “Castillo-Morales palatal plate,” which is
provided for cerebral palsy patients. The movable rolling bead must be
placed where the patient’s tongue touches the palate during swallowing.
The bead can be placed either on the side of the palate, or in the middle
– depending on the child’s swallowing pattern.
Inga CJ, Reddy AK, Richardson SA, Sanders B: Appliance for chronic
drooling in cerebral palsy patients. Pediatric Dentistry. May 2001; 23:(3)
241-242